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Синдром Когана – новая нозология в современной классификации системных васкулитов. Клиническое наблюдение и обзор литературы

https://doi.org/10.14412/1995-4484-2016-463-468

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Аннотация

Представлено клиническое наблюдение типичного варианта синдрома Когана (СК) – новой нозологической формы современной классификации системных васкулитов (СВ), принадлежащей к группе вариабельных васкулитов. В обзоре литературы подробно освещены проблемы диагностики и лечения этого редкого заболевания.

СК характеризуется воспалительным поражением глаз (интерстициальный кератит, увеит, эписклерит) и патологией органа слуха (нейросенсорная тугоухость, вестибулярные нарушения) с возможным развитием васкулита другой локализации, аортита, поражения аортального и митрального клапанов. Системное поражение с вовлечением ЛОР-органов и глаз требует исключения гранулематоза с полиангиитом (Вегенера) и дифференциальной диагностики с широким спектром заболеваний. Представленные данные подчеркивают необходимость междисциплинарного сотрудничества ревматологов, оториноларингологов, аудиологов, офтальмологов, кардиологов для совершенствования диагностики и лечения этой формы СВ. 

Об авторе

Т. В. Бекетова
ФГБНУ Научно- исследовательский институт ревматологии им. В.А. Насоновой, Москва
Россия

115522 Москва, Каширское шоссе, 34А 



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Для цитирования:


Бекетова Т.В. Синдром Когана – новая нозология в современной классификации системных васкулитов. Клиническое наблюдение и обзор литературы. Научно-практическая ревматология. 2016;54(4):463-468. https://doi.org/10.14412/1995-4484-2016-463-468

For citation:


Beketova T.V. Cogan's syndrome is a new nosological entity in the current classification of systemic vasculitides: A clinical case and a review of literature. Rheumatology Science and Practice. 2016;54(4):463-468. (In Russ.) https://doi.org/10.14412/1995-4484-2016-463-468

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ISSN 1995-4484 (Print)
ISSN 1995-4492 (Online)